ISSN: 1300-7777 E-ISSN: 1308-5263
Aortic aneurysm and non-Hodgkin’s lymphoma in Marfan syndrome [Turk J Hematol]
Turk J Hematol. 2009; 26(1): 31-33

Aortic aneurysm and non-Hodgkin’s lymphoma in Marfan syndrome

Sujoy Ghosh, Subrata Ghosh, Sandip Kumar Ghosh
The Ayr Hospital, Scotland, Uk

The combination of Marfan syndrome with lymphoma is extremely rare. This report describes a case of Marfan syndrome who presented with chest discomfort and was diagnosed to have an aortic aneurysm and an additional incidental mediastinal mass that on further investigation turned out to be a diffuse large B cell lymphoma. We have suggested a hypothesis which can explain the occurrence of lymphoma in Marfan syndrome.

Keywords: Marfan syndrome, non-Hodgkin's Lymphoma, aortic aneurysm, TGF-beta, Fibrillin


Marfan sendromunda Hodgkin dışı lenfoma ve aort anevrizması

Sujoy Ghosh, Subrata Ghosh, Sandip Kumar Ghosh
The Ayr Hospital, Scotland, Uk

Marfan sendromu ile lenfoma kombinasyonu oldukça enderdir. Bu rapor, göğüs rahatsızlığı ile gelen ve aort anevrizması ve tesadüfen ilave bir mediastinal kitlesi olduğu tespit edilen bir Marfan sendromu olgusunu anlatmaktadır. Daha ileri bir tetkik ile bu mediastinal kitlenin diffüz büyük B hücreli lenfoma olduğu açığa çıkmıştır. Marfan sendromunda lenfoma oluşumunu açıklayabilen bir hipotez ileri sürdük.

Anahtar Kelimeler: Marfan sendromu, Hodgkin dışı lenfoma, aort anevrizması, TGF-beta, Fibrillin


Sujoy Ghosh, Subrata Ghosh, Sandip Kumar Ghosh. Aortic aneurysm and non-Hodgkin’s lymphoma in Marfan syndrome. Turk J Hematol. 2009; 26(1): 31-33

Corresponding Author: Sujoy Ghosh, United Kingdom


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