ISSN: 1300-7777 E-ISSN: 1308-5263
Polycythemia Vera Presenting with Fulminant Hepatic Failure Due to Acute Budd-Chiari Syndrome: Case Report [Turk J Hematol]
Turk J Hematol. 2002; 19(1): 43-45

Polycythemia Vera Presenting with Fulminant Hepatic Failure Due to Acute Budd-Chiari Syndrome: Case Report

Süleyman Sami Kartı1, Mustafa Yılmaz1, Elif Altun2, Polat Koşucu3, Mehmet Arslan4, Ercüment Ovalı1
1Department Of Hematology, School Of Medicine, Karadeniz Technical University, Trabzon, Turkey
2Department Of Internal Medicine, School Of Medicine, Karadeniz Technical Univers, Trabzon, Turkey
3Department Of Radiology, School Of Medicine, Karadeniz Technical University, Trabzon, Turkey
4Department Of Gastroenterology, School Of Medicine, Karadeniz Technical University, Trabzon, Turkey

We describe a 38 year-old woman with polycythemia vera who presented with fulminant hepatic failure due to acute Budd-Chiari syndrome. She had a history of abdominal pain and distention for 4 days. Laboratory and clinical findings showed fulminant hepatic failure due to acute Budd-Chiari syndrome. Diagnosis was confirmed with abdominal ultrasonography and doppler ultrasonography showing ascites, hepatomegaly, portal hypertension and total occlusion of hepatic veins. Complete blood count and other clinical findings were compatible with polycythemia vera. The patient was successfully treated with urgent administration of continuous heparin infusion, repeated phlebotomies and hydroxyurea. We emphasize that early diagnosis and effective treatment in such fulminant cases can be life saving.

Keywords: Budd-Chiari syndrome, Polycythemia vera, Hepatic failure.


Süleyman Sami Kartı, Mustafa Yılmaz, Elif Altun, Polat Koşucu, Mehmet Arslan, Ercüment Ovalı. Polycythemia Vera Presenting with Fulminant Hepatic Failure Due to Acute Budd-Chiari Syndrome: Case Report. Turk J Hematol. 2002; 19(1): 43-45

Corresponding Author: Süleyman Sami Kartı, Türkiye


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